Resumo

ANDRADE ALBAN, Noemí Rocío et al. Ebstein anomaly: a case report. Vive Rev. Salud [online]. 2025, vol.8, n.23, pp.781-789.  Epub 01-Maio-2025. ISSN 2664-3243.  https://doi.org/10.33996/revistavive.v8i23.411.

Ebstein's anomaly is a complex and rare congenital defect that includes morphophysiological malformations of the tricuspid valve and right ventricle. It occurs in 1 in 200,000 live births and represents 1% of congenital heart diseases. It is frequently associated with other defects such as: interatrial septum, pulmonary stenosis or atresia, ventricular septal defect, aortic coarctation, and tetralogy of Fallot. A 49-year-old patient with a history of Ebstein's anomaly and congestive heart failure reports dyspnea on heavy exertion since school age, without other accompanying symptoms. Approximately 15 days ago, the condition worsened to dyspnea on moderate exertion accompanied by palpitations, atypical chest pain, and asthenia, which is why the decision was made to admit him. An echocardiogram showed a low-set tricuspid valve in the right ventricle. An electrocardiogram revealed atrial fibrillation, complete right bundle branch block, and ventricular repolarization disorder. The patient is progressing favorably; however, given the complications associated with Ebstein's anomaly, expectant and palliative pharmacological treatment was decided upon. Ebstein's anomaly represents a cardiac malformation with a low incidence rate. Echocardiography is considered the preferred modality for detecting the disease due to its ability to provide visual confirmation of tricuspid valve abnormality.

Palavras-chave : Ebstein's anomaly; Congenital heart disease; Tricuspid valve.

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