Resumen

COLQUE MAMANI, Wilfor German  y  MALDONADO GOMEZ, Alejandra Belen. HERLYN-WERNER WUNDERLICH SYNDROME. CLINICAL CASE PRESENTATION. Rev Cient Cienc Méd [online]. 2023, vol.26, n.2, pp.104-109.  Epub 31-Dic-2023. ISSN 1817-7433.

Herlyn-Werner-Wunderlich syndrome (HWWS), a rare müllerian and mesonephric malformation, is characterized by a didelphic uterus, obstructed hemivagina and ipsilateral renal anomalies. Although the precise incidence is uncertain, it constitutes 0.1% to 3.5% of Müllerian anomalies. We present a clinical case of a 13-year-old female adolescent with abdominal pain and radiological diagnosis of HWWS. Surgical intervention revealed a partially obstructed bicornuate uterus, hematometra and acute appendicitis, with additional findings such as splenomegaly and left monorrhea. Management included transuterine evacuation and appendectomy. The discussion highlights the rarity of the syndrome and its possible complications, while the conclusion highlights the importance of the multidisciplinary approach in the diagnosis and treatment of HWWS, emphasizing collaboration between gynecologists, surgeons and radiologists.

Palabras clave : Syndrome; Hematocolpos; Agenesis.

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