Abstract

MEJIA-ESCOBAR, Cinthya Karina; SANCHEZ-SIERRA, Luis Enrique  and  SALGADO, Ana Luisa. PARRY-ROMBERG SYNDROME: PROGRESSIVE FACIAL HEMIATROPHY. CASE REPORT. Rev Cient Cienc Méd [online]. 2020, vol.23, n.2, pp.262-266. ISSN 1817-7433.

Introduction: Parry-Romberg Syndrome is a neurocutaneous disorder, very rare and characterized by progressive facial hemiatrophy, the first clinical sign is facial asymmetry. SPR occurs simultaneously with high frequency with linear scleroderma. Case presentation: A 54-year-old female,with a history of left facial hemiatrophy since she was 14 years old, presented a left ophthalmological alteration. Discussion: Parry-Romberg Syndrome begins in the first decades of life with hyperpigmentation, atrophy of the dermis, subcutaneous fat, muscle and underlying bones. Atrophic affects the hemicara with distribution of the trigeminal nerve and its branches; this case coincided with the age of onset and the lesion was limited to the left hemicra. Conclusion: It should be borne in mind as a differential diagnosis in patients with long-standing facial symmetry alteration without apparent cause, early diagnosis avoids serious complications, multidisciplinary management is recommended to improve the quality of life of patients.

Keywords : Parry-Romberg Syndrome; Facial hemiatrophy; Neurocutaneous disorder.

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