Resumo

DAVID-MURILLO, Perla; LAGOS-RIVERA, Samuel; SUAZO-VILLALOBOS, Daniel  e  BU, Efrain. Caroli's Disease: Presentation of a case. Rev Cient Cienc Méd [online]. 2015, vol.18, n.2, pp.53-56. ISSN 2077-3323.

Caroli disease is a rare congenital condition, which incidence is estimated at 1 case per million. Characterized by saccular or fusiform dilation of the bile. Clinical manifestations include right upper quadrant pain, fever and jaundice, these crisis of cholangitis are secondary to biliary stasis, and sepsis. Diagnosis is based on the discovery of cystic lesions in biliary tree, it may be seen by ultrasound, computed tomography. We present a case of female patient with 37-year-old, who attends to the emergency service of internal medicine of the Hospital Escuela Universitario of the city ofTegucigalpa, Honduras, manifesting signs and symptoms of acute cholangitis and jaundice. Physical examination reveals globose and painful abdomen at the expense of a marked he-patomegaly. Our patient presented episodes of recurrent cholangitis, the computed tomography reveals multiple cystic spaces in both lobes and was found lesions in the biliary tree. Excluding, sclerosing cholangitis, hydatid cyst, bile duct and hereditary ductal dilatation, and confirmed the suspected diagnosis of Caroli's disease.

Palavras-chave : Caroli disease; Cholangitis; Cholestasis; Bile ducts.

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