Abstract

ANDIA BERAZAIN, Cinthya  and  SANZ ARRAZOLA, Heydi. Impact of West Syndrome in Patients from Manuel Ascencio Villarroel's Children Hospital. Rev Cient Cienc Méd [online]. 2014, vol.17, n.2, pp.9-13. ISSN 1817-7433.

West syndrome is a pediatric epileptic encephalopathy dependent on age characterized by the classic triad of epileptic spasms and mental retardation hypsarrhythmic pattern. It begins in most patients during the 1 st year of life, with an incidence between 3 and 12 months of age. Presents various etiologies: cryptogenic, idiopathic and symptomatic. The aim of the research is to describe the clinical presentation of West syndrome the diagnosis and treatment used. The study is descriptive and cross-sectional.The universe comprises 377 patients younger than 2 years with epilepsy who attended the clinic of Pediatric Neurology Children's Hospital Manuel AscencioVillarroelViedma Hospital in Cochabamba, Bolivia, January 1, 2010 to December 31,2013. The shows are the 12 patients who were diagnosed with West syndrome. In the results emerged: the 12 patients met the classic triad of the disease, with 100% symptomatic, corresponding to 8 and 4 female to male. The age at which the diagnosis is most often made was 9 to 12 months. 5 cases with preterm pregnancy and 6 cases with perinatal asphyxia:evaluation of prenatal and neonatal history including highlights was performed. Computed tomography and electroencephalogram: Additional diagnostic tests were performed. It is concluded that the clinical presentation of West syndrome in our country is symptomatic in 12 cases found, the diagnosis was based on clinical and complementary examinations. Treatment is mainly used valproic acid because the adrenocorticotropic hormone is not available in our country.

Keywords : West syndrome; spasms ¡nfantile; hypsarrhythmia.

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