Abstract

FERNANDEZ POBLETE, Higinia; SALGUEIRO FERNANDEZ, Wendy Rayza  and  RODAS ILLANES, Jose Israel. PENTALOGY OF CANTRELL ASSOCIATED WITH ECTOPIA CORDIS: REPORT OF A CASE. Rev. Méd. La Paz [online]. 2014, vol.20, n.1, pp.49-52. ISSN 1726-8958.

The Pentalogy of Cantrell is a rare set of abnormalities that includes a supraumbilical abdominal wall defect, agenesis of the anterior portion of the diaphragm, absence of the diaphragmatic pericardium and cardiac malformation. We present a description of the monitoring of a case of a patient of 32 years, with apparently normal pregnancy, with fetal movements slightly decreased during the course of pregnancy, and maternal blood pressure slightly elevated. An ultrasound detected severe oligohidramnios and congenital malformations corresponding to Pentalogy of Cantrell. Ending the pregnancy due to the diagnosis is decided wisely to practice cesarean. One hour prior to cesarean the patient reports fetal movements not perceived. By the surgical procedure is obtained a unique product alive, without weeping, little movement members, that only lives about 30 seconds, presenting the aforementioned characteristics of the Pentalogy of Cantrell associated with ectopia cordis, and other anomalies subsequent to these.

Keywords : Pentalogy of Cantrell; Ectopia Cordis; Omphalocele.

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