Gaceta Médica Boliviana
Print version ISSN 1012-2966
The kidney malformation is not hereditary, it could be unilateral or less frequently, bilateral, sometimes is segmental. It corresponds to the kidney cystic Potter type II. The dysfunction affects the bifurcation of the bud ureteral in its first generations, the one that expands without inducing the nefrones formation. The dilatations constitute cysts of diverse sizes that on the whole give to the kidney the form of a cluster of grapes. The urine is not formed . Microscopically they are islands of heterotopic embryonic fabrics, as cartilage, hematopoiesis tisue and others. When it is bilateral it is incompatible with the life and associates to the Potter facies. In half of the cases there are other malformations. When it is unilateral usually shows in the mature age for complications like infections, lithiasis or hematuria.
Keywords : Multicystic kidney disease; unilateral; Potter type II.